Criss cross heart; a challenging diagnosis, case series

Authors

  • Abdul Malik Sheikh Department of Pediatric Cardiology, Rawalpindi Institute of Cardiology, Rawalpindi, Pakistan
  • Asma Kanwal Department of Pediatric Cardiology, Rawalpindi Institute of Cardiology, Rawalpindi, Pakistan
  • Hina Sattar Department of Pediatrics, District Headquarter Hospital, Rawalpindi, Pakistan

DOI:

https://doi.org/10.47391/JPMA.3162

Abstract

Crisscross heart (CCH) is a rare anomaly characterized by twisting of the inflow streams of right and left ventricles. The etiology of CCH is not known. Its frequency is less than 8/10, 00,000 live births. Cyanosis is common in neonatal age, while shortness of breath is the main presenting complaint in older children. We present a case series of CCH with array of associations, diagnosed by echocardiography.

CCH is a rare heart defect that can be diagnosed by echocardiography by a vigilant operator. Early diagnosis is the key to successful management resulting in increased survival rate, better outcomes and improved quality of life.

Keywords: Criss-Cross heart, mitral valve lesions, coarctation of aorta, Echocardiography, case series.

Additional Files

Published

2022-02-19

How to Cite

Sheikh, A. M., Asma Kanwal, & Hina Sattar. (2022). Criss cross heart; a challenging diagnosis, case series. Journal of the Pakistan Medical Association. https://doi.org/10.47391/JPMA.3162

Issue

Section

Case Series